Neonatal stridor in familial congenital Laryngeal Paralysis (Plott Syndrome) : a case study in an Omani family
Joint Authors
Shatla, Imad Sadik
Prashanth, Gowda Parameshwara
Aguiar, Rodney
al-Haqq, Adl Ahmad
Shivalingam, Ganji
Source
Issue
Vol. 32, Issue 6 (30 Nov. 2017), pp.432-434, 3 p.
Publisher
Publication Date
2017-11-30
Country of Publication
Oman
No. of Pages
3
Main Subjects
Abstract EN
Stridor presenting soon after birth due to bilateral abductor vocal cord paralysis (VCP) is rare.
We report a family with bilateral VCP affecting four male members in two generations and hence suggesting X-linked recessive inheritance.
Severe stridor in the neonatal period requires meticulous airway evaluation, and tracheostomy in 35–70% cases.
The current trend is towards conservative management and tracheostomy is avoided unless respiratory distress is severe or life-threatening.
Neonatal VCP can be an isolated finding, or it can be familial with or without syndromic features.
There are very few reports of non-syndromic familial cases.
Unlike the cases reported previously, none of our patients required prolonged intubation or tracheostomy suggesting an excellent prognosis in such cases.
This is the first case study of congenital familial non-syndromic VCP reported from the Middle East.
American Psychological Association (APA)
Shatla, Imad Sadik& Prashanth, Gowda Parameshwara& Aguiar, Rodney& Shivalingam, Ganji& al-Haqq, Adl Ahmad. 2017. Neonatal stridor in familial congenital Laryngeal Paralysis (Plott Syndrome) : a case study in an Omani family. Oman Medical Journal،Vol. 32, no. 6, pp.432-434.
https://search.emarefa.net/detail/BIM-772623
Modern Language Association (MLA)
Shatla, Imad Sadik…[et al.]. Neonatal stridor in familial congenital Laryngeal Paralysis (Plott Syndrome) : a case study in an Omani family. Oman Medical Journal Vol. 32, no. 6 (Nov. 2017), pp.432-434.
https://search.emarefa.net/detail/BIM-772623
American Medical Association (AMA)
Shatla, Imad Sadik& Prashanth, Gowda Parameshwara& Aguiar, Rodney& Shivalingam, Ganji& al-Haqq, Adl Ahmad. Neonatal stridor in familial congenital Laryngeal Paralysis (Plott Syndrome) : a case study in an Omani family. Oman Medical Journal. 2017. Vol. 32, no. 6, pp.432-434.
https://search.emarefa.net/detail/BIM-772623
Data Type
Journal Articles
Language
English
Record ID
BIM-772623