Ewing sarcomas of the Sino-nasal tract and maxillary bone

Abstract EN

Ewing’s sarcoma is a malignant tumor belonging to the group of small round cells tumors.

Histologically similar to soft tissue neoplasms originally described as primitive neuroectodermal tumors (PNET), in the WHO classification, Ewing’s sarcoma and PNET are labeled together under the rubric of EWS/PNET.

Rarely located in the nasal cavity and the para-nasal sinuses, we report three cases of Ewing’s sarcoma of maxillary bone and sinus.

Our patients, 2 males and one female, were aged 20, 16 and 13 years respectively.

The chief complaint was a painful face swelling.

The diagnosis was retained on histologic and immuno-histochemical results.

In two cases, surgery was performed as primary treatment modality followed by chemo-radiotherapy, which was the only therapeutic modality in the remaining case.

After a follow-up of 2, 3 and 8 years (for each patient), we did not report local or distant failures.