A case report of pseudoxanthoma elasticum-like papillary dermal elastolysis

Abstract EN

Pseudoxanthoma elasticum-like papillary dermal elastolysis is a relatively rare disorder within the literature.

Increased awareness of this entity will broaden the diff erential diagnoses among dermatologists encountering such a condition.

Pseudoxanthoma elasticum-like papillary dermal elastolysis tends to occur predominantly in elderly females.

Clinically, the lesions present as papules and cobblestone plaques on the neck, resembling pseudoxanthoma elasticum.

Histologically, there is absence of elastic fi bers in the papillary dermis, and no calcifi cation of the remaining fi bers.

Pseudoxanthoma elasticum-like papillary dermal elastolysis diff ers from Pseudoxanthoma elasticum by the absence of systemic manifestations, hence patients are reassured and no further workup is warranted.

As of now, no eff ective treatments are available for this entity.

Pseudoxanthoma elasticum-like papillary dermal elastolysis should be in the diff erential diagnosis of a dermatologist when encountering a clinical presentation of Pseudoxanthoma elasticum in an elderly patient localized to the neck, with absence of fragmented and calcifi ed elastic fi bers on histologic examination.